Young girl with Kawasaki disease

Abstract

Kawasaki disease (KD) is an acute multisystem necrotizing vasculitis of unknown etiology involving medium-size vessels. It usually occurs in young children between 1 to 5 years of age. The diagnosis of classic KD is based on the simultaneous presence of high fever for 5 or more days with at least four of the remaining five symptoms which includes non-purulent bilateral conjunctivitis, changes in the lips or oral cavity, cervical lymphadenopathy, polymorphous exanthema, desquamation of the peripheral extremities. We present a case of a 4 years old girl who presented with history of fever, pain in multiple joints, oral and lip ulcers and peeling off of her skin on her palms and soles. She was started on aspirin and intravenous immunoglobulins (IVIG) to which she responded very well and was asymptomatic within a week. She had initially been managed empirically elsewhere for infection for over 2 months. Her echocardiography was normal and despite having delayed diagnosis and management, did not develop any cardiac complications.